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Table 1 Patient characteristics

From: Pheochromocytoma and Paraganglioma in Neurofibromatosis type 1: frequent surgeries and cardiovascular crises indicate the need for screening

Total number of patients

17

Gender (male/female)

9/8

Average age at diagnosis (years, range)

41 (20–62)

Means of diagnosis (biochemical/imaging/unknown)

5/11/1

Incidental Imaging finding (yes/no)

8/9

Presence of cardiovascular crisis (# patients)

6

Hypertension (yes/no/unknown)

9/8/0

Tachycardia, HR > 100 (yes/no/unknown)

4/5/5

Both HTN & Tachycardia (yes/no/unknown)

2/10/5

Number antihypertensive medications (average, range)

1 (0–4)

Elevated plasma or urine catecholamines or metanephrines (yes/no/unknown)

16/0/1

Level of metanephrine elevation (times upper limit of normal). (mean/median/range)

 

UM

UNM

PM

PNM

12.6/ 5.2/ (0.5–19.0)

4.6/ 2.7/ (0.6–3.5)

6.7/ 3.6/ (0.7–16.8)

3.2/ 2.0/ (1.4–10.2)

Elevations in both metanephrines & normetanephrines (yes/no/unknown)

10/1/6

MIBG scan (pos/neg/not done)

9/0/8

  1. Abbreviations: HTN hypertension, HR heart rate, UM (urine metanephrine, reference range < 300 mcg/24 h), UNM (urine normetanephrine, reference range < 800 mcg/24 h), PM (plasma metanephrine, reference range < 0.5 nmol/L), PNM (plasma normetanephrine, reference range < 0.9 nmol/L), MIBG meta-iodobenzylguanidine